Anaesthetic Management for VP Shunt Insertion in an Infant with Dandy-Walker Syndrome

Dandy–Walker Syndrome (DWS) is a rare congenital brain anomaly affecting the cerebellum and the fourth ventricle.The chief components of the syndrome include cystic dilatation of the fourth ventricle and agenesis or hypoplasia of the cerebellar vermis. These abnormalities are typically associated with hydrocephalus.Patients often present in infancy for cerebrospinal fluid shunt procedures. Anaesthetic management of patients with DWS may prove challenging due to the frequent association of abnormalities in other systems. Airway management may also prove to be difficult.