Congenital Epidermolysis Bullosa with Pyloric Atresia

Epidermolysis bullosa (EB) comprises a group of genetically determined skin fragility disorders, which are characterised by blistering of the skin and mucosa, in response to little or no apparent trauma. Among the sub-types, EB with pyloric atresia is particularly rare form of EB even more so is EB with duodenal atresia. Herein, we report a case of EB associated with congenital duodenal atresia.