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Anaesthetic Management of Amniotic Band Syndrome: A Case Report


Affiliations
1 Department of Anaesthesiology and Critical Care, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India
 

Amniotic Band Syndrome (ABS) is a complex congenital condition caused by strands of amniotic sac associated with a broad spectrum of anomalies. It is also known as amniotic band sequence, Amniotic Deformity, Adhesions, Mutilations (ADAM) complex, congenital constriction rings, constriction band syndrome, limb body wall complex, Streeter anomaly, Streeter dysplasia, Annular grooves, Congenital amputation, Pseudoainhulm[1]. The abnormalities vary from isolated to multiple bizarre disfiguring complications involving craniofacial region, limbs and visceral organs. General anaesthesia is the preferred choice for surgical correction of anomalies.

Keywords

Amniotic Band Syndrome, High Arched Palate, Syndactyly.
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  • Anaesthetic Management of Amniotic Band Syndrome: A Case Report

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Authors

V. Shobha
Department of Anaesthesiology and Critical Care, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India
Veena Asthana
Department of Anaesthesiology and Critical Care, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India
Amit Kumar Chauhan
Department of Anaesthesiology and Critical Care, Himalayan Institute of Medical Sciences, Dehradun, Uttarakhand, India

Abstract


Amniotic Band Syndrome (ABS) is a complex congenital condition caused by strands of amniotic sac associated with a broad spectrum of anomalies. It is also known as amniotic band sequence, Amniotic Deformity, Adhesions, Mutilations (ADAM) complex, congenital constriction rings, constriction band syndrome, limb body wall complex, Streeter anomaly, Streeter dysplasia, Annular grooves, Congenital amputation, Pseudoainhulm[1]. The abnormalities vary from isolated to multiple bizarre disfiguring complications involving craniofacial region, limbs and visceral organs. General anaesthesia is the preferred choice for surgical correction of anomalies.

Keywords


Amniotic Band Syndrome, High Arched Palate, Syndactyly.

References