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Posterior Urethral Valve Syndrome: An Uncommon Cause of Intrauterine Fetal Death


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1 Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
     

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A posterior urethral valve is an obstructing membrane in the posterior part of male urethra leading to renal failure and death occurring in 1:5000 to 8000 male live births. The incidence of intrauterine deaths related to posterior urethral valve is under reported. The cause for the occurrence is unclear. Posterior Urethral Valve syndrome is a syndrome of obstructive uropathy resulting in hypertrophy of bladder, ureters and dysplasia of the kidneys. Prenatal ultrasonography is a gold standard diagnostic tool. The fetal autopsy conducted over the case presented here demonstrates all the classical findings of the obstructive uropathy (renal dysplasia, hydronephrosis, bladder hypertrophy, hydro ureters). The case reiterates the importance of prenatal ultrasonography and meticulous fetal autopsy to determine the cause of intra uterine fetal death.

Keywords

Posterior Urethral Valve Syndrome, Obstructive Uropathy, Fetal Autopsy, Intrauterine Death
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  • Posterior Urethral Valve Syndrome: An Uncommon Cause of Intrauterine Fetal Death

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Authors

G. Mahesh
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
O. Murugesa Bharathi
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
K. M. Roop Kumar
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
S. Sudhakar
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
S. Sreedhar Reddy
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India
Uday Pal Singh
Department of Forensic Medicine, Mamata Medical College, Khammam, Andhra Pradesh, India

Abstract


A posterior urethral valve is an obstructing membrane in the posterior part of male urethra leading to renal failure and death occurring in 1:5000 to 8000 male live births. The incidence of intrauterine deaths related to posterior urethral valve is under reported. The cause for the occurrence is unclear. Posterior Urethral Valve syndrome is a syndrome of obstructive uropathy resulting in hypertrophy of bladder, ureters and dysplasia of the kidneys. Prenatal ultrasonography is a gold standard diagnostic tool. The fetal autopsy conducted over the case presented here demonstrates all the classical findings of the obstructive uropathy (renal dysplasia, hydronephrosis, bladder hypertrophy, hydro ureters). The case reiterates the importance of prenatal ultrasonography and meticulous fetal autopsy to determine the cause of intra uterine fetal death.

Keywords


Posterior Urethral Valve Syndrome, Obstructive Uropathy, Fetal Autopsy, Intrauterine Death

References