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Mccune-Albright Syndrome


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1 Deputy Nursing Officer, SRI Ramakrishna Hospital, Coimbatore – 44, India
     

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McCune-Albright syndrome is a rare and challenging congenital sporadic disease involving the skin and skeletal and endocrine systems. In addition to the classical triad of fibrous dysplasia of bone, cafe au lait pigmented skin lesions and precocious puberty, other multiple endocrinological features, including hyperthyroidism, growth hormone excess, hypercortisolism, and hypophosphatemic rickets, have been reported. A brief review of the syndrome in children is here reported.

Keywords

McCune–Albright Syndrome, Endocrinopathies, Precocious Puberty Cafe au lait Skin Pigmentation, Fibrous Dysplasia of Bone.
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  • Mccune-Albright Syndrome

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Authors

P. A. Rejini
Deputy Nursing Officer, SRI Ramakrishna Hospital, Coimbatore – 44, India

Abstract


McCune-Albright syndrome is a rare and challenging congenital sporadic disease involving the skin and skeletal and endocrine systems. In addition to the classical triad of fibrous dysplasia of bone, cafe au lait pigmented skin lesions and precocious puberty, other multiple endocrinological features, including hyperthyroidism, growth hormone excess, hypercortisolism, and hypophosphatemic rickets, have been reported. A brief review of the syndrome in children is here reported.

Keywords


McCune–Albright Syndrome, Endocrinopathies, Precocious Puberty Cafe au lait Skin Pigmentation, Fibrous Dysplasia of Bone.

References