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Undifferentiated Embryonal Sarcoma of the Liver in an Adult Patient:Case Report with Review of Literature


Affiliations
1 Oscar Superspeciality Hospital and Trauma Centre, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
2 Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
3 Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
4 Department of Radiodiagnosis, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
5 Department of Obstetrics and Gynaecology, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, India
     

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We present a case of undifferentiated embryonal sarcoma of liver (UESL), a rare and aggressive tumour with poor prognosis. It is an uncommon hepatic tumour, of mesenchymal origin, usually observed in children, and cases in adults are rare. We present a case in a 22 year old healthy male with only mild abdominal pain. On admission the patient had normal aspartate aminotransferase, alanine aminotransferase. He also tested negative for hepatitis and tumour markers. On Computed tomography (CT) scan a large solid cystic mass was seen which was diagnosed as UESL on immunohistochemistry.

Keywords

Embryonal Sarcoma, Liver, Immunohistochemistry, Computed Tomography.
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  • Undifferentiated Embryonal Sarcoma of the Liver in an Adult Patient:Case Report with Review of Literature

Abstract Views: 254  |  PDF Views: 1

Authors

N. Jain
Oscar Superspeciality Hospital and Trauma Centre, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
S. Magu
Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
R. Yadav
Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
S. Rohilla
Department of Radiodiagnosis, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, Haryana, India
S. Jain
Department of Obstetrics and Gynaecology, Pt. BD Sharma, PGIMS, University of Health Sciences, Rohtak, India

Abstract


We present a case of undifferentiated embryonal sarcoma of liver (UESL), a rare and aggressive tumour with poor prognosis. It is an uncommon hepatic tumour, of mesenchymal origin, usually observed in children, and cases in adults are rare. We present a case in a 22 year old healthy male with only mild abdominal pain. On admission the patient had normal aspartate aminotransferase, alanine aminotransferase. He also tested negative for hepatitis and tumour markers. On Computed tomography (CT) scan a large solid cystic mass was seen which was diagnosed as UESL on immunohistochemistry.

Keywords


Embryonal Sarcoma, Liver, Immunohistochemistry, Computed Tomography.

References