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Lissencephaly-'Who Should be Diagnosing It?'


Affiliations
1 Cloudnine Hospitals, India
2 Cloudnine Hospitals, Bangalore, India
     

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Lissencephaly is a rare congenital developmental brain disorder resulting from defect in neuronal migration, leading to a characteristic marked reduction or absence of the convolution pattern of the cerebral hemispheres. The paucity in the development of brain gyri and sulci is due to defective neuronal migration during 10-14 weeks. We report a lissencephaly case, in 33 weeks+5days twins with refractory seizures and review the literature regarding the same.

Keywords

Lissencephaly, Neuronal Migration.
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  • Lissencephaly-'Who Should be Diagnosing It?'

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Authors

R. K. Kumar
Cloudnine Hospitals, India
S. V. Girish
Cloudnine Hospitals, Bangalore, India
P. C. Nayana Prabha
Cloudnine Hospitals, Bangalore, India
K. S. Gill
Cloudnine Hospitals, Bangalore, India

Abstract


Lissencephaly is a rare congenital developmental brain disorder resulting from defect in neuronal migration, leading to a characteristic marked reduction or absence of the convolution pattern of the cerebral hemispheres. The paucity in the development of brain gyri and sulci is due to defective neuronal migration during 10-14 weeks. We report a lissencephaly case, in 33 weeks+5days twins with refractory seizures and review the literature regarding the same.

Keywords


Lissencephaly, Neuronal Migration.

References