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Hypokalemic Periodic Paralysis and Renal tubular Acidosis as Presenting Manifestation of Primary Sjogren’s Syndrome - A Case Report


Affiliations
1 department of neurology, Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India
2 department of internal medicine, Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India
3 department of neurology Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India
     

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Among wide list of differentials of periodic paralysis, hypokalemia is an important cause. However hypokalemia with respiratory failure as sole presenting feature of Sjogren’s syndrome (SS) is rarely reported. We report a case of recur-rent hypokalemic paralysis which presented with life threatening respiratory failure in second episode, hypokalemia was found due to distal renal tubular acidosis and on further investigation diagnosis of primary SS was made. In this article we emphasize need for detailed work-up of a case of recurrent hypokalemic periodic paralysis in order to iden-tify the underlying etiology and do timely management in order to avoid future recurrence.

Keywords

Hypokalemic Periodic Paralysis, Sjogren’s Syndrome, Quadriparesis.
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  • Hypokalemic Periodic Paralysis and Renal tubular Acidosis as Presenting Manifestation of Primary Sjogren’s Syndrome - A Case Report

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Authors

Saurabh Gupta
department of neurology, Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India
Shikha Gupta
department of internal medicine, Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India
Naushad Ravjani
department of neurology Pacific Medical College and Hospital, Udaipur, Rajasthan - 313011, India

Abstract


Among wide list of differentials of periodic paralysis, hypokalemia is an important cause. However hypokalemia with respiratory failure as sole presenting feature of Sjogren’s syndrome (SS) is rarely reported. We report a case of recur-rent hypokalemic paralysis which presented with life threatening respiratory failure in second episode, hypokalemia was found due to distal renal tubular acidosis and on further investigation diagnosis of primary SS was made. In this article we emphasize need for detailed work-up of a case of recurrent hypokalemic periodic paralysis in order to iden-tify the underlying etiology and do timely management in order to avoid future recurrence.

Keywords


Hypokalemic Periodic Paralysis, Sjogren’s Syndrome, Quadriparesis.

References