Rosai Dorfman Disease

Rosai Dorfman disease or Sinus histiocytosis with massive lymphadenopathy (SHML) is a benign, self-limiting disorder that commonly presents as massive bilateral and painless cervical lymphadenopathy. We present a case of a 6 year old male child who presented with cervical lymphadenopathy with no other complaints and was diagnosed on fine needle aspiration cytology as a case of Rosai Dorfman disease. Patient was given low dose steroids and he responded well to become asymptomatic by 15 days.