Indian Journal of Public Health Research & Development

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Primary Extraskeletal Ewing's Sarcoma of Nasal Cavity


Affiliations
1 Dept. of Pathology, Navodaya Medical College, Raichur, Karnataka
     

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Extra skeletal Ewing's Sarcoma (EES) of nasal cavity is a rare soft tissue tumor, morphologically similar to the commoner Ewing's sarcoma (ES) arising from bone. We report a case of EES of nasal cavity in a nine year old male who presented with nasal obstruction. Contrast enhanced CT scan showed mildly enhancing soft tissue attenuating mass. Histopathologically examination showed round cell tumor which was confirmed by special stain and immunohistochemistry. PAS showed positivity for intracellular glycogen, Immunohistochemistry showed positivity for MIC-2, CK, S- 100, EMA.

An extensive review of literature, to the best of our knowledge, did not reveal many cases of EES of nasal cavity, in children younger than ten years


Keywords

ES, Primitive Neuroectodermal Tumor ( PNET ), Nasal cavity, Children
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  • Primary Extraskeletal Ewing's Sarcoma of Nasal Cavity

Abstract Views: 474  |  PDF Views: 0

Authors

A S Anand
Dept. of Pathology, Navodaya Medical College, Raichur, Karnataka
V R Chandrakanth
Dept. of Pathology, Navodaya Medical College, Raichur, Karnataka
C M Sagar
Dept. of Pathology, Navodaya Medical College, Raichur, Karnataka
Vidisha Athanikar
Dept. of Pathology, Navodaya Medical College, Raichur, Karnataka

Abstract


Extra skeletal Ewing's Sarcoma (EES) of nasal cavity is a rare soft tissue tumor, morphologically similar to the commoner Ewing's sarcoma (ES) arising from bone. We report a case of EES of nasal cavity in a nine year old male who presented with nasal obstruction. Contrast enhanced CT scan showed mildly enhancing soft tissue attenuating mass. Histopathologically examination showed round cell tumor which was confirmed by special stain and immunohistochemistry. PAS showed positivity for intracellular glycogen, Immunohistochemistry showed positivity for MIC-2, CK, S- 100, EMA.

An extensive review of literature, to the best of our knowledge, did not reveal many cases of EES of nasal cavity, in children younger than ten years


Keywords


ES, Primitive Neuroectodermal Tumor ( PNET ), Nasal cavity, Children

References