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Congenital Ranula with Caroli's Syndrome in an Infant: A Rare Case Report


Affiliations
1 Department of Pedodontics & Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India
2 Department of Department of Pedodontics & Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India
 

Ranulas are cystic dilatations in the floor of the mouth and a result of obstruction of one of the sublingual salivary glands. It is basically a retention cyst. Ranula may be congenital or acquired. Caroli's disease is a rare communicating segmental or diffuse dilatation of the intrahepatic biliary tree, Cholangitis, liver cirrhosis and cholangio-carcinoma are its potential complications. Congenital ranula in newborn infants is a rarity and thus there is a marked paucity of the literature on the cited subject. This article is an interesting case report of a patient presenting with ranula in a rare syndrome called Caroli's syndrome.

Keywords

Congenital Ranula, Infant, Salivary Gland, Caroli's Syndrome.
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  • Congenital Ranula with Caroli's Syndrome in an Infant: A Rare Case Report

Abstract Views: 414  |  PDF Views: 114

Authors

K. B. Roopa
Department of Pedodontics & Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India
P. Poornima
Department of Department of Pedodontics & Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India
Meghna Bajaj
Department of Pedodontics & Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India

Abstract


Ranulas are cystic dilatations in the floor of the mouth and a result of obstruction of one of the sublingual salivary glands. It is basically a retention cyst. Ranula may be congenital or acquired. Caroli's disease is a rare communicating segmental or diffuse dilatation of the intrahepatic biliary tree, Cholangitis, liver cirrhosis and cholangio-carcinoma are its potential complications. Congenital ranula in newborn infants is a rarity and thus there is a marked paucity of the literature on the cited subject. This article is an interesting case report of a patient presenting with ranula in a rare syndrome called Caroli's syndrome.

Keywords


Congenital Ranula, Infant, Salivary Gland, Caroli's Syndrome.

References





DOI: https://doi.org/10.15636/jdp%2F2014%2Fv1i2%2F60739