Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13‑year‑old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.
Keywords
Hyperkeratosis, lamellar ichthyosis, skin scaling
User
Font Size
Information