Karnataka Anaesthesia Journal

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Anaesthetic Management of Kartageners Syndrome Posted for Kasai Surgery


Affiliations
1 Department of Anesthesia, Bangalore Medical College and Research Institute, Bengaluru - 560002, Karnataka, India
 

Kartagener's syndrome is a rare autosomal recessive disorder presenting with a triad of sinusitis, bronchicetasis and situs inversus with dextrocardia. It occurs in 50% of patients with situs inversus .Patients with genetic disorders associated with multiple congenital anomalies present unique challenges to the anesthesiologist. We report the successful intraoperative management of a child with biliary atresia, situs inversus totalis, and Kartegener syndrome scheduled for corrective biliary surgery. We recommend that patients with multiple congenital anomalies need to be thoroughly and cautiously evaluated.

Keywords

Anesthesia, Biliary Atresia, Hepatobiliary Surgery, Situs Inversus Totalis
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  • Anaesthetic Management of Kartageners Syndrome Posted for Kasai Surgery

Abstract Views: 59  |  PDF Views: 51

Authors

Saraswathi Nagapaa
Department of Anesthesia, Bangalore Medical College and Research Institute, Bengaluru - 560002, Karnataka, India
Sandhya Kalappa
Department of Anesthesia, Bangalore Medical College and Research Institute, Bengaluru - 560002, Karnataka, India

Abstract


Kartagener's syndrome is a rare autosomal recessive disorder presenting with a triad of sinusitis, bronchicetasis and situs inversus with dextrocardia. It occurs in 50% of patients with situs inversus .Patients with genetic disorders associated with multiple congenital anomalies present unique challenges to the anesthesiologist. We report the successful intraoperative management of a child with biliary atresia, situs inversus totalis, and Kartegener syndrome scheduled for corrective biliary surgery. We recommend that patients with multiple congenital anomalies need to be thoroughly and cautiously evaluated.

Keywords


Anesthesia, Biliary Atresia, Hepatobiliary Surgery, Situs Inversus Totalis

References