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A Case of Congenital Pulmonary Airway Malformation


Affiliations
1 Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
     

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Congenital pulmonary airway malformations (CPAM) are considered part of the spectrum of bronchopulmonary foregut malformations. Diagnosis is usually made during the antenatal period and is rarely diagnosed in adults. The spectrum of clinical presentations varies from asymptomatic cases to recurrent respiratory tract infections or respiratory insufficiency in adulthood. Here we report one such case of an elderly female who presented with a history of recurrent respiratory tract infections and associated respiratory dysfunction since childhood. The aim of this article is to highlight a case of CPAM because of its rarity, especially in adulthood, and to briefly discuss the subtypes and differential diagnosis of cystic lung diseases of childhood.

Keywords

Congenital Pulmonary Airway Malformation, Congenital Cystic Adenomatoid Malformation, Cystic Lung Diseases.
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  • A Case of Congenital Pulmonary Airway Malformation

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Authors

R. Dheeraj
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
S. Amitha
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
S. Sanjeev
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
R. Chetambath
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India

Abstract


Congenital pulmonary airway malformations (CPAM) are considered part of the spectrum of bronchopulmonary foregut malformations. Diagnosis is usually made during the antenatal period and is rarely diagnosed in adults. The spectrum of clinical presentations varies from asymptomatic cases to recurrent respiratory tract infections or respiratory insufficiency in adulthood. Here we report one such case of an elderly female who presented with a history of recurrent respiratory tract infections and associated respiratory dysfunction since childhood. The aim of this article is to highlight a case of CPAM because of its rarity, especially in adulthood, and to briefly discuss the subtypes and differential diagnosis of cystic lung diseases of childhood.

Keywords


Congenital Pulmonary Airway Malformation, Congenital Cystic Adenomatoid Malformation, Cystic Lung Diseases.

References