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A Case of Congenital Pulmonary Airway Malformation


Affiliations
1 Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
     

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Congenital pulmonary airway malformations (CPAM) are considered part of the spectrum of bronchopulmonary foregut malformations. Diagnosis is usually made during the antenatal period and is rarely diagnosed in adults. The spectrum of clinical presentations varies from asymptomatic cases to recurrent respiratory tract infections or respiratory insufficiency in adulthood. Here we report one such case of an elderly female who presented with a history of recurrent respiratory tract infections and associated respiratory dysfunction since childhood. The aim of this article is to highlight a case of CPAM because of its rarity, especially in adulthood, and to briefly discuss the subtypes and differential diagnosis of cystic lung diseases of childhood.

Keywords

Congenital Pulmonary Airway Malformation, Congenital Cystic Adenomatoid Malformation, Cystic Lung Diseases.
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  • Ch’in KY, Tang MY. Congenital adenomatoid malformation of one lobe of a lung with general anasarca. Arch Pathol (Chic) 1949;48:221–29. [PubMed]

  • Adzick NS, Harrison MR, Glick PL, Golbus MS, Anderson RL, Mahony BS, et al. Fetal cystic adenomatoid malformation: prenatal diagnosis and natural history. J Pediatr Surg. 1985; 20:483–88. [PubMed]

  • Berrocal T, Madrid C, Novo S, Arjonilla A, Gomez-Leon N. Congenital anomalies of the tracheobronchial tree, lung, and mediastinum: embryology, radiology, and pathology. Radiographics 2004;24:e17. [PubMed]

  • Cass DL, Quinn TM, Yang EY, Liechty KW, Crombleholme TM, Flake AW. Increased cell proliferation and decreased apoptosis characterize congenital cystic adenomatoid malformation of the lung. J PediatrSurg 1998; 33(7):1043-46[Medline].

  • Gross GW. Pediatric chest imaging. CurrOpinRadiol 1992;4 (5): 36-43. (Pubmed)

  • Priest JR, Williams GM, Hill DA, Dehner LP, Jaffé A. Pulmonary cysts in early childhood and the risk of malignancy. Pediatr. Pulmonol. 2009;44 (1): 14-30. (Pubmed)

  • Granata C, Gambini C, Balducci T, Toma P, Michelazzi A, Conte M. Bronchioloalveolar carcinoma arising in congenital cystic adenomatoid malformation in a child: a case report and review on malignancies originating in congenital cystic adenomatoid malformation. PediatrPulmonol. 1998; 25(1):6266 [Medline].

  • Oh BJ, Lee JS, Kim JS, Lim CM, Koh Y. Congenital cystic adenomatoid malformation of the lung in adults: clinical and CT evaluation of seven patients. Respirology 2006;11 (4):496501.

  • AnningFeng, HourongCai, Qi Sun, Yifen Zhang, Lulu Chen, FanqingMeng. Congenital cystic adenomatoid malformation of lung in adults: 2 rare cases report and review of the literature. DiagnPathol. 2012; 7: 37-40 (Pubmed).


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  • A Case of Congenital Pulmonary Airway Malformation

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Authors

R. Dheeraj
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
S. Amitha
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
S. Sanjeev
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India
R. Chetambath
Dept. of Pulmonary Medicine, DM Wayanad Institute of Medical Sciences, Wayanad, Kerala, India

Abstract


Congenital pulmonary airway malformations (CPAM) are considered part of the spectrum of bronchopulmonary foregut malformations. Diagnosis is usually made during the antenatal period and is rarely diagnosed in adults. The spectrum of clinical presentations varies from asymptomatic cases to recurrent respiratory tract infections or respiratory insufficiency in adulthood. Here we report one such case of an elderly female who presented with a history of recurrent respiratory tract infections and associated respiratory dysfunction since childhood. The aim of this article is to highlight a case of CPAM because of its rarity, especially in adulthood, and to briefly discuss the subtypes and differential diagnosis of cystic lung diseases of childhood.

Keywords


Congenital Pulmonary Airway Malformation, Congenital Cystic Adenomatoid Malformation, Cystic Lung Diseases.

References