Indian Journal of Forensic Medicine & Toxicology

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Camurati Engelmann’s Disease (CED): A Case Report


Affiliations
1 G.G.S.Medical College & Hospital (BFUHS) Faridkot, Punjab, India
2 Maharaja Agrasen Medical College, Agroha, Hisar, India
     

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Camurati Engelmann's disease is rare and is characterized by severe limb pain, proximal muscle weakness and hyperostosis of long bones and the skull. We report a case of Camurati Engelmann's disease with decreased muscle mass and weakness. There was increased lumbar lordosis, calcaneovalgus of both feet and enlargement of shafts of femur and tibia. Diagnosis was established on X-rays which showed hyperostosis of both femur and tibia and sclerosis of skull bones. The child was put on corticosteroids and analgesics and there was alleviation of symptoms after two follow-ups.

Keywords

Camurati-engelmann’s Disease, Lumbar Lordosis, Hyperostosis, Corticosteroids.
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  • Camurati Engelmann’s Disease (CED): A Case Report

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Authors

Amit Thakur
G.G.S.Medical College & Hospital (BFUHS) Faridkot, Punjab, India
Vishali Kotwal
G.G.S.Medical College & Hospital (BFUHS) Faridkot, Punjab, India
Rahul Agrawal
Maharaja Agrasen Medical College, Agroha, Hisar, India
Manpreet Kaur Bajwa
Maharaja Agrasen Medical College, Agroha, Hisar, India

Abstract


Camurati Engelmann's disease is rare and is characterized by severe limb pain, proximal muscle weakness and hyperostosis of long bones and the skull. We report a case of Camurati Engelmann's disease with decreased muscle mass and weakness. There was increased lumbar lordosis, calcaneovalgus of both feet and enlargement of shafts of femur and tibia. Diagnosis was established on X-rays which showed hyperostosis of both femur and tibia and sclerosis of skull bones. The child was put on corticosteroids and analgesics and there was alleviation of symptoms after two follow-ups.

Keywords


Camurati-engelmann’s Disease, Lumbar Lordosis, Hyperostosis, Corticosteroids.

References