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Camurati Engelmann’s Disease (CED): A Case Report
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Camurati Engelmann's disease is rare and is characterized by severe limb pain, proximal muscle weakness and hyperostosis of long bones and the skull. We report a case of Camurati Engelmann's disease with decreased muscle mass and weakness. There was increased lumbar lordosis, calcaneovalgus of both feet and enlargement of shafts of femur and tibia. Diagnosis was established on X-rays which showed hyperostosis of both femur and tibia and sclerosis of skull bones. The child was put on corticosteroids and analgesics and there was alleviation of symptoms after two follow-ups.
Keywords
Camurati-engelmann’s Disease, Lumbar Lordosis, Hyperostosis, Corticosteroids.
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